Innovative Journal Innovative Journal of Medical and Health Science 2455-3549 07 03 2021 3 3 VON ZUMBUSCH PSORIASIS: A BRIEF REPORT 1 André Nazário de Oliveira Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Rodolfo Borges Franco de Macêdo Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Sandra Maíra Carrijo Marques Palma Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Raquel Marques Sandri Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Cristhenise Ragnini Silva UNIFACIMED - Faculty of Biomedical Sciences of Cacoal- cristhiany Ragnini Oliveira Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Kelli Fabiane Moreira Laboranalises - Clinical Laboratory Lucas Chiarato Fernandes UNIFACIMED - Faculty of Biomedical Sciences of Cacoal- Wulgner Farias Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Eliane Costa de Oliveira Coelho Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Mahler Giordani Mileo Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Guilherme Eler de Almeida Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia RafaelCavatti Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Flávio de Jesus Junior Medical Residency Program – Internal Medicine/Regional Hospital of Cacoal-Rondônia Ketlin Batista Morais Mendes Medical Residency Program in Gastroenterology – Getúlio Vargas University Hospital/Manaus-Amazonas Journal Article https://doi.org/10.15520/arjmcs.v7i03.263 Abstract Psoriasis is a chronic non-contagious inflammatory disease present in up to 3% of the population. As for the forms of presentation, it can be classified into: vulgar or in plaques (most common manifestation), in drops or gutta, erythrodermic, pustular or arthropathic. Moreover, some atypical cases stand out, such as acute pustular psoriasis namely Von Zumbusch. Systemic complications, such as heart failure and diseases, can be fatal. Next, we report the case of a patient with Von Zumbusch's pustular psoriasis admitted to our service and admitted for clinical investigation. Thais Jerez, Jaime, Beatriz Alessi Rodrigues; Tatiana Jerez Jaime; Maria Lourdes Peris Barbo; Deborah Regina Cunha Simis. Psoríase de von Zumbusch, An Bras Dermatol, 2009, 84, 3, 299, 301 Thais Jerez, Jaime, Beatriz Alessi Rodrigues; Tatiana Jerez Jaime; Maria Lourdes Peris Barbo; Deborah Regina Cunha Simis. Psoríase de von Zumbusch, An Bras Dermatol, 2009, 84, 3, 299, 301 Sampaio, Sap, Rivitti, E A, Dermatologia, São Paulo: Artes Medicas, 2007, 3, 227, 268 - Van Der Kerkhof, Pcm, Psoriasis, Dermatology. New York: Mosby, 2003, 125, 151 FRITSCH, P., Oral Retinoids in Dermatology, International Journal of Dermatology, 1981, 20, 5, 314, 329, 0011-9059, 1365-4632, 10.1111/j.1365-4362.1981.tb00814.x, Wiley, https://dx.doi.org/10.1111/j.1365-4362.1981.tb00814.x Ettler, Karel, Richards, Bernard, Acitretin therapy for palmoplantar pustulosis combined with UVA and topical 8-MOP, International Journal of Dermatology, 2001, 40, 8, 541, 542, 0011-9059, 1365-4632, 10.1046/j.1365-4362.2001.01094-3.x, Wiley, https://dx.doi.org/10.1046/j.1365-4362.2001.01094-3.x Marrakchi, S, Guigue, P, Renshaw, B R, Interleukin-36-receptor antagonist deficiency and generalized pustular psoriasis, N Engl J Med, 2011, 365, 7, 620, 628 Onoufriadis, A, Simpson, M A, Pink, A E, Mutations in IL36RN/IL1F5 are associated with the severe episodic inflammatory skin disease known as generalized pustular psoriasis, Am J Hum Genet, 2009, 89, 3, 432, 437 Johnston, A, Xing, X, Wolterink, L, IL-1 and IL-36 are dominant cytokines in generalized pustular psoriasis, J Allergy Clin Immunol, 2017, 140, 1, 109, 120 Benjegerdes, K E, Hyde, K, Kivelevitch, D, Mansouri, B, Pustular psoriasis: pathophysiology and current treatment perspectives. Psoriasis: Targets and Therapy, 2016, 6, 131, 144